In many cases, the two kidneys are fused together, yet retain their own vessels and ureters. Although the initial clinical suspicion was a tumoral. Crossed fused renal ectopia is a rare congenital anomaly, and is mostly. Agenesis or ectopia of the kidney is frequently accompanied by characteristic malposition of specific portions of the bowel. Abdominal aortic aneurysm associated with crossed renal ectopia. An ectopic kidney may remain in the pelvis, near the bladder pelvic kidney. Ectopic kidneys renal ectopia causes, symptoms, diagnosis, complications, treatment in india, ectopic kidneys it may remain undetected in the absence of. A rare association of crossed fused renal ectopia bmc. Patients with crossed renal ectopia often have other organ and system malformations. Often, the crossed kidney is fused with the uncrossed kidney, from the online textbook of urology by d. To report two cases of right crossed nonfused renal ectopia diagnosed in male patients about 30 years of age who arrived to emergency centres with symptoms of renal colic. Crossed fused renal ectopia with a single ureter and single renal vein is a rare congenital anomaly in which both the fused kidneys lie on one side of the body. Ectopic kidney is a birth defect in which a kidney is located at an abnormal location.
This survey was conducted to study the clinical profile and the challenges posed in the management of this entity. Ureteral ectopia medigoo health medical tests and free. Jun 03, 2015 this illustrations deals with one of the important renal anomalies, ectopic kidney. Crossed fused renal ectopia with renal calculus and gross hydronephrosis a case report author. Bladder exstrophy is a congenital anomaly that exists along the spectrum of the exstrophyepispadias complex, and most notably involves protrusion of the urinary bladder through a defect in the abdominal wall. Apr 04, 2017 renal ectopy and fusion are common congenital anomalies of the kidney and urinary tract cacut. Most cases of renal ectopia remain asymptomatic during a persons lifetime and are diagnosed incidentally. Crossed fused renal ectopia is the fusion of both kidneys, with at least one kidney on the side opposite its normal location incidence 17000 births 1. Following a contrastenhanced ct scan, a right to left cross fused ectopic kidney was identified with the right kidney overlying the inferior vena. Crossed fused kidney ectopia is a very rare congenital malformation. Pancake kidney is one of the rarest types of renal ectopia. We report an unusual presentation of a case of crossed renal ectopia without fusion. It results from the kidney failing to ascend from its origin in the true pelvis or from a superiorly ascended kidney located in the thorax.
Blood biochemistry was within normal limits and her kidneyureterbladder xray revealed no abnormality. An ectopic kidney, also known as renal ectopia, is a congenital renal anomaly characterized by the abnormal location of one or both of the kidneys. Thought to result from aberrant metanephros development in which the normal displacement of the fetal kidneys from the pelvis to the lumbar fossae is altered or inhibited. Crossed renal ectopia is one of the rarest urinary system anomalies. This anomaly has not been previously reported in association with tar syndrome. Simple renal ectopia refers to a kidney thats located on the proper side but in an abnormal position. Ectopic kidney is a congenital defect that results due to improper positioning of the kidney during fetal development. An ectopic kidney may cross over and can become fused with the other kidney crossed renal ectopia.
Crossed fused renal ectopia of the superior ectopia type leylaakdogan, 1,2 alikemaloguz, 1,2 tarkanergun, 3,4 andihsanergun 5 department of internal medicine, ufuk university school of medicine, ankara, turkey. Crossed fused renal ectopia is a very rare anomaly in which both kidneys are located on the same side and are fused. In this case, a male patient was admitted to our hospital because of doublelimb edema, hematuria and proteinuria and all preoperative examinations indicated that the left kidney is ectopic to. Ectopia vesicae definition of ectopia vesicae by the free. Congenital renal fusion and ectopia in the trauma patient. An adult lady diagnosed as a case of ovarian carcinoma, found to have a mass in the left thoracic cavity. We present two separate cases of young male patients with congenital kidney anomalies horseshoe and crossed fused renal ectopia identified following blunt abdominal trauma. Aug 22, 2017 sistema excretorurinario os rins e a filtragem do sangue anatomia humana videoaula 030 duration. Jun, 2019 criptorquidia y ectopia testicular pdf criptorquidia.
We report an unusual case of nonfused crossed renal ectopia. Pdf crossed fused renal ectopia with a single ureter. Pdf crossed fused renal ectopia with repeated kidney and. Xray of the kidney, ureters and bladders revealed stonefree status. Percutaneous nephrolithotomy pcnl in renal fusion, ectopia, renal rotational anomalies, renal hypoplasia, and pelvicaliceal aberration for complex calculi is challenging for fear of inaccessibility, vascular, colonic, and splanchnic injury. The two leading causes of urinary incontinence in dogs are ureteral ectopia in juveniles and urethral sphincter mechanism incompetence in adults. Crossed renal ectopia without fusionan unusual cause of. Ectopic kidney renal ectopia causes, symptoms, diagnosis. Crossed fused renal ectopia with single ureter and. Both kidneys are located on the same side of the body. All structured data from the file and property namespaces is available under the creative commons cc0 license. We report a case of tar syndrome with crossed fused renal ectopia. Information here will help you talk with your urologist if you or your child has an ectopic kidney. Crossed renal ectopia is a rare congenital malformations where a kidney is located on the side opposite to side of its urethral insertion into the urinary bladder and is generally fused with the normally located ipsilateral kidney.
Our patient is a 16yearold adolescent male, previously fit and healthy, who presented with acute onset of abdominal pain. Management of upper urinary tract calculi in crossed fused renal. It may remain undetected in the absence of abdominal pain or urinary infection. Since these pathologies are frequently asymptomatic, the diagnosis is most commonly madeafter a routine imaging studies due to other causes or when recurrent uti or urinary obstruction are associated. The kidney is separated from the pleural cavity by a thin membrane in continuity of the diaphragm. Incidental renal findings may influence the management of. We report the first patient of tar syndrome associated with crossed fused renal ectopia and discuss the pathogenetic explanation for crossed fused renal ectopia. Crossed fused renal ectopia is a rare congenital malformation, which is reported to be usually asymptomatic but may have varied presentations. The upper pole of the left pelvic kidney in the male impinged upon a lateral bony projection from the body of the 5th lumbar vertebra. Focused assessment with sonography in trauma to search for free. Renal ectopia diagnostic imaging gomal journal of medical sciences julydecember 2008, vol.
Crossed renal ectopia is said to be present when the kidney is seen in the opposite retroperitoneal space. While the accuracy of diagnosis of ectopic ureters. Renal agenesis and ectopia dynamic radiology barnard. Renal ectopia synonyms, renal ectopia pronunciation, renal ectopia translation, english dictionary definition of renal ectopia. Crossed renal ectopia is a rare congenital malformation and is the second most common fusion anomaly after a horseshoe kidney. Crossed renal ectopia with fusion in a female feline.
The incidence of renal ectopia is 1 in 400 cases of autopsy and 85% of these occur with a fused kidney. Ectopic kidney describes a kidney that is not located in its usual position. Most cases are asymptomatic and remain undiagnosed. Renal ectopia definition of renal ectopia by medical. The code is valid for the year 2020 for the submission of hipaacovered transactions. To date, ureteral ectopia combined with renal dysplasia and urolithiasis has not been documented. Fusion anomalies fas of the kidneys are divided into crossed fused ectopia cfe and horseshoe kidney hk. Ureteral ectopia is often present in combination with other urinary abnormalities, such as hydroureter, hydronephrosis, pyelonephritis, bladder hypoplasia, and the presence of an intrapelvic bladder neck associated with a short urethra. This illustrations deals with one of the important renal anomalies, ectopic kidney. Crossed renal ectopia is the location of the kidney on the contralateral side in respect to the ureteral orfice location in the bladder. Abstract among the anomalies of the upper urinary tract are the anomalies of ascent, which includes simple renal ectopia, and the anomalies of form and fusioninclude, which s crossed renal. Pdf crossed fused renal ectopia is a rare congenital malformation, which is.
As each kidney ascends, it rotates through 90 degrees such that the renal hilum is directed medially as the kidney reaches its final position. Since ureteral ectopia frequently arises in a duplicated, and often hydronephrotic, renal system,3,10 highdose delayed ivp is often helpful in visualizing the ectopic ureter. Simple renal ectopia is the abnormal position of the kidney outside of the renal fossa in cranial or caudal direction. Crossed fused renal ectopia cfre is a rare congenital anomaly in which. It is more common for the left kidney to be ectopically located on the right side. If the kidney crosses to the other side of the body, it is called crossed renal ectopia. Crossed renal ectopia cre is a rare congenital anomaly that is. Crossed renal ectopia is one of the rarest congenital malformations where a kidney is located on the side. Issn 23214287 305 original article crossed fused renal ectopia multidetector computed tomography study sharma v 1, ramesh babu c. Crossed fused renal ectopia radiology reference article. Renal ectopia definition of renal ectopia by medical dictionary.
Crossed renal ectopia is a congenital anomaly which usually goes unnoticed as most cases are asymptomatic. Thoracic ectopic kidney is a rare anomaly, the rarest of all renal ectopia types 0. The underlying embryologic mechanism leading to bladder exstrophy is unknown. Crossed renal ectopia is a rare congenital anomaly in which the kidneys are located on the same side, whereas the ureter of the ectopic kidney still descends to the normal location on the bladder. A rare association of crossed fused renal ectopia article pdf available in bmc nephrology 81. The first patient was free of stones after three sessions, while the second patient.
A cyst was present at the lower pole of the same kidney. Laparoscopic nephrolithotomy in a patient with crossed. Renal ectopia is often linked to birth defects in other organ systems. Crossed fused renal ectopia multidetector computed tomography study sharma v 1, ramesh babu c. Crossed fused renal ectopia is a rare congenital anomaly, and is. The 11yearold adolescent female patient was admitted with abdominal pain, anorexia, weight loss, and periumbilical mass. Crossed fused renal ectopia refers to an anomaly where the kidneys are fused and located on the same side of the midline. If reflux into the ureteral ectopia is present, resection of distal ectopic ureter is necessary. Crossed fused renal ectopia with renal calculus and gross. Bilateral pelvic kidneys and a unilateral pelvic kidney were found in a male and female cadaver, respectively. Crossed ectopic kidneys are fused to their ipsilateral mate in 90% of cases.
Company logo congenital abnormalities kidney and urinary tract 2. Abdominopelvic ultrasonography and intravenous urography had revealed lefttoright crossed fused renal ectopia with a 25 mm opaque stone in the crossed kidney. An ectopic kidney is a kidney that does not grow in the proper location. Crossed fused renal ectopia essentially refers to an anomaly where the kidneys are fused and located on the same side of the midline. We report a rare case of crossed renal ectopia presenting with pain abdomen unusual. Crossed renal ectopia is a rare type of congenital malformation of the urinary system that shares a 12000 incidence. In this patient, due to the crossed renal ectopia, the course of the ureter was unclear. The results showed evidence of a renal mass which was diagnosed as an ectopic kidney through computed tomography ct. Rapid caudal growth results in the migration of the developing kidney from the pelvis to the retroperitoneal renal fossa, which lies on either side of the spine opposite the second lumbar vertebra. Thrombocytopenia and absent radius syndrome tar is a rare genetic disorder. Its presentation is variable, often including abnormalities of the bony pelvis, pelvic floor, and genitalia. It is an autosomal recessive disorder characterised by radial aplasia and thrombocytopenia that may have additional anomalies. Crossed renal ectopia has been commonly described as four different variants, including bilateral crossed renal ectopia, sshaped kidney, lshaped kidney, and disc kidney 3. Ectopia lentis is a displacement or malposition of the eyes crystalline lens from its normal location.
Crossed fused renal ectopia with a single ureter and single renal vein is a rare congenital anomaly in which both the fused kidneys lie on one. Crossed renal ectopia refers to a kidney that has crossed from its side, to the other side. About 20% of patients with crossed renal ectopia also have vur guarino et al. Dysgenesis of the kidney a renal agenesisabsent kidney b renal hypoplasia c renal dysplasia 2. It can be a simple uncrossed ectopia in which one or both the kidneys are ectopic in position and in some cases a kidney is located. When the kidney stays in the pelvis, it is called a pelvic kidney. More than 85% of these get fused resulting in crossed fu. More than 85% of these get fused resulting in crossed fused renal ectopia. Article pdf available february 2017 with 830 reads. Common sheat ureteroneocystostomy ucn for a duplex kidney with closely spaced ureteral orifices. Ureteropyelostomy or ureteroureterostomy for a duplex kidney and widely spaced ureteral orifices. Dec 15, 2019 agenesis or ectopia of the kidney is frequently accompanied by characteristic malposition of specific portions of the bowel. We report 2 cases that illustrate these difficulties and show that a branch artery stenosis may be overlooked even by the gold standard method, renal angiography obesity is a risk factor for renal damage in native kidney disease and in renal transplant recipients.
Rodriguez faba and others published ectopia renal cruzada. A partial dislocation of a lens is termed lens subluxation or subluxated lens. Pdf to report two cases of right crossed nonfused renal ectopia. We saw a case of crossed renal ectopia without fusion, a rare anomaly. Crossed renal ectopia is a rare congenital anomaly most often silent. Pdf a rare association of crossed fused renal ectopia. We report a case of pancake kidney which was detected incidentally while treating a female patient for a urinary tract infection.
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